Treatment

Tetralogy of Fallot can be treated by:

1. Several palliative surgical procedures are described which involve detouring flow from the aorta to the pulmonary artery (via a surgically created shunt) to enhance pulmonary artery flow.
2. There is no definitive medical therapy.
3. Polycythemia can be treated with hydroxyurea (50 mg/kg PO QOD) to suppress bone marrow production of RBCs.

If arrhythmias are present, manage as per pulmonic stenosis. Beta blocker therapy is recommended by some, efficacy is unsubstantiated. Intermittent phlebotomies may manage some of the symptoms of Tetralogy of Fallot.